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Dernières publications
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Valentina Taglietti, Kaouthar Kefi, Lea Rivera, Oriane Bergiers, Nastasia Cardone, et al.. Thyroid-stimulating hormone receptor signaling restores skeletal muscle stem cell regeneration in rats with muscular dystrophy. Science Translational Medicine, 2023, 15 (685), ⟨10.1126/scitranslmed.add5275⟩. ⟨hal-04150315⟩
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A. Morin, Amalia Stantzou, Olga N. Petrova, John C.W. Hildyard, T. Tensorer, et al.. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle. Proceedings of the National Academy of Sciences of the United States of America, 2023, 120 (2), ⟨10.1073/pnas.2206324120⟩. ⟨hal-04122777⟩
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Valentina Taglietti, Kaouthar Kefi, Iwona Bronisz-Budzyńska, Busra Mirciloglu, Mathilde Rodrigues, et al.. Duchenne muscular dystrophy trajectory in R-DMDdel52 preclinical rat model identifies COMP as biomarker of fibrosis. Acta Neuropathologica Communications, 2022, 10 (1), ⟨10.1186/s40478-022-01355-2⟩. ⟨hal-03828280⟩
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Chiffres clés
48
Publications avec texte intégral
Open Access
67 %
Mots clés
LncARN
Multiresolution modeling
Becker muscular dystrophy
Energy Metabolism/drug effects
Becker BMD muscular dystrophy
Inbred mdx
LKB1
Inhibitors
Morphogenesis
Muscular Atrophy
Dystrophy
Becker muscular dystrophy BMD
Muscle
CTNNB1
CaVβs
Dystrophin-EGFP
Long noncoding RNA
L-Type
Calcium Channels
DMD
Drp1
Humans
Dystrophie Musculaire de Becker BMD
Genomic
Multi exon skipping
Dystrophin
Myotendinous junction
Dystrophine
Gene modifiers
Duchenne muscular dystrophy
Duchenne DMD dystrophy
Mdx mouse
Hear
Human Umbilical Vein Endothelial Cells
Muscle Biology
Cell homeostasis
Modificateurs de gènes
Liver
Mice
Multi resolution modeling
Animals
Cardiomyopathy
Skeletal muscle
LncRNA
Homeostasis
Hepatocellular carcinoma
Long QT
Calcium
Muscular Dystrophy
Muscle development
Knockout
Myogenesis
Exon skipping
Activin Receptors
Base Sequence
Cachexia
CD38
Cell Biology
Clinical trials
Autophagy
Dystrophin central domain
Animal/physiopathology
Muscles/physiopathology
Metabolism
Dystrophie Musculaire de Duchenne DMD
Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS
Muscular dystrophy
Duchenne muscular dystrophy DMD
Muscle Strength
Inbred C57BL
Molecular Sequence Data
NAD+
Génomique
Cell Line
Delivery
NNOS
MES
Dystrophie musculaire de Becker
DHPR α1S
Molecular docking
Mitochondrial fission
Male
Diseases
Gene expression
Antisense oligonucleotides
CaV subunits
BMD
DMO
Allele‐specific silencing therapy
Dynamin 2
Cardiomyopathie
Epigenetics
Cells
Centronuclear myopathy
Cultured
MiARN
Invivo
Immunoglobulin Fc Fragments/pharmacology
Gene Expression Regulation/drug effects
Ex-vivo